# OnCo record appendiceal (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix owl: <http://www.w3.org/2002/07/owl#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/appendiceal/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "appendiceal" ;
  schema:name "Appendiceal cancer and pseudomyxoma peritonei"@en ;
  schema:alternateName "Appendix cancer"@en, "PMP"@en, "Low-grade appendiceal mucinous neoplasm (LAMN)"@en ;
  schema:description "Rare tumours of the appendix that range from slow mucin-producing growths that fill the abdomen (pseudomyxoma peritonei) to aggressive adenocarcinomas. The slow forms are treated by extensive surgery with heated chemotherapy in the abdomen; the fast ones like colon cancer."@en ;
  schema:url <https://onco.cc/cancers/appendiceal/> ;
  schema:dateModified "2026-09-08"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Pseudomyxoma_peritonei> ;
  owl:sameAs <http://www.wikidata.org/entity/Q574694> ;
  schema:citation <https://doi.org/10.1097/PAS.0000000000000535>, <https://www.acpmp.org/> ;
  onco:tag "gap-fill", "gastrointestinal", "rare" ;
  onco:technologies <https://onco.cc/technologies/hipec/>, <https://onco.cc/technologies/cytotoxic-chemotherapy/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/mri/> ;
  onco:targets <https://onco.cc/targets/kras/>, <https://onco.cc/targets/tp53/> ;
  onco:drugs <https://onco.cc/drugs/folfox/>, <https://onco.cc/drugs/capox/>, <https://onco.cc/drugs/bevacizumab/>, <https://onco.cc/drugs/mitomycin/> ;
  onco:pathways <https://onco.cc/pathways/ras-mapk/> ;
  onco:terms <https://onco.cc/terms/peritoneal-metastasis/>, <https://onco.cc/terms/colectomy/> ;
  onco:pipeline <https://onco.cc/technologies/hipec/>, <https://onco.cc/drugs/folfox/> ;
  onco:standardOfCare <https://onco.cc/drugs/folfox/>, <https://onco.cc/drugs/capox/>, <https://onco.cc/technologies/hipec/>, <https://onco.cc/drugs/folfox/>, <https://onco.cc/drugs/capox/>, <https://onco.cc/drugs/bevacizumab/> .
