# OnCo record choroid-plexus-carcinoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/choroid-plexus-carcinoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "choroid-plexus-carcinoma" ;
  schema:name "Choroid plexus carcinoma"@en ;
  schema:alternateName "Choroid plexus carcinoma (WHO grade 3)"@en, "Malignant choroid plexus tumour"@en, "CPC"@en ;
  schema:description "Choroid plexus carcinoma is a rare, aggressive brain tumour of infants and young children that grows from the tissue that makes spinal fluid inside the brain's ventricles, causing fluid build-up and pressure. It is strongly linked to an inherited TP53 fault (Li-Fraumeni syndrome), so families are tested; treatment is surgery, then chemotherapy and, in older children, radiotherapy."@en ;
  schema:url <https://onco.cc/cancers/choroid-plexus-carcinoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Choroid_plexus_carcinoma> ;
  schema:citation <https://www.cancer.gov/types/childhood-cancers/patient/rare-childhood-cancers-pdq>, <https://doi.org/10.3171/2012.8.peds12132>, <https://doi.org/10.1002/pbc.23349>, <https://doi.org/10.1002/cncr.25826> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/brain-tumours/>, <https://onco.cc/cancers/childhood-cancers/>, <https://onco.cc/cancers/pineoblastoma/>, <https://onco.cc/cancers/atrt/>, <https://onco.cc/cancers/adrenocortical/> ;
  onco:technologies <https://onco.cc/technologies/germline-testing/> ;
  onco:targets <https://onco.cc/targets/tp53/> ;
  onco:drugs <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/carboplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/cyclophosphamide/> ;
  onco:terms <https://onco.cc/terms/li-fraumeni/> ;
  onco:standardOfCare <https://onco.cc/cancers/brain-tumours/>, <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/technologies/germline-testing/>, <https://onco.cc/terms/li-fraumeni/> .
