# OnCo record del5q (term). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/terms/del5q/>
  a schema:DefinedTerm ;
  onco:kind "term" ;
  schema:identifier "del5q" ;
  schema:name "del(5q) (5q- syndrome and lenalidomide response)"@en ;
  schema:alternateName "del(5q)"@en, "5q deletion"@en, "5q-"@en, "5q minus"@en, "5q- syndrome"@en, "5q minus syndrome"@en, "MDS with isolated del(5q)"@en, "MDS-5q"@en, "isolated del(5q)"@en, "del 5q MDS"@en, "chromosome 5q deletion syndrome"@en, "MDS with low blasts and isolated 5q deletion"@en ;
  schema:description "Losing a piece of the long arm of chromosome 5 causes a distinctive low-risk myelodysplastic syndrome, typically an older woman with severe anaemia and a normal or high platelet count; it is the one MDS with a drug matched to its genetics, lenalidomide, which makes two-thirds of patients transfusion-free unless TP53 is also mutated."@en ;
  schema:url <https://onco.cc/terms/del5q/> ;
  schema:dateModified "2026-09-17"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Chromosome_5q_deletion_syndrome> ;
  schema:citation <https://en.wikipedia.org/wiki/Chromosome_5q_deletion_syndrome> ;
  onco:related <https://onco.cc/terms/ipss-m-ipss-r/>, <https://onco.cc/terms/cytogenetics/>, <https://onco.cc/terms/fish/>, <https://onco.cc/drugs/lenalidomide/>, <https://onco.cc/targets/cereblon/>, <https://onco.cc/terms/tp53-mutated/>, <https://onco.cc/drugs/luspatercept/> ;
  onco:cancers <https://onco.cc/cancers/mds-lower-risk/>, <https://onco.cc/cancers/mds-higher-risk/> .
