# OnCo record dermatofibrosarcoma-protuberans (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/dermatofibrosarcoma-protuberans/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "dermatofibrosarcoma-protuberans" ;
  schema:name "Dermatofibrosarcoma protuberans"@en ;
  schema:alternateName "DFSP"@en, "Bednar tumour (pigmented dermatofibrosarcoma protuberans)"@en, "Fibrosarcomatous dermatofibrosarcoma protuberans"@en ;
  schema:description "Dermatofibrosarcoma protuberans is a rare, slow-growing cancer of the deeper skin that usually appears as a firm plaque or lump on the trunk and is often mistaken for a scar or cyst for years. Surgery with wide margins cures most people; for the few whose tumour cannot be removed or has spread, the pill imatinib works because almost every one is driven by a single gene fusion it blocks."@en ;
  schema:url <https://onco.cc/cancers/dermatofibrosarcoma-protuberans/> ;
  schema:dateModified "2026-09-17"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Dermatofibrosarcoma_protuberans> ;
  schema:citation <https://ascopubs.org/doi/10.1200/JCO.2009.25.9899>, <https://en.wikipedia.org/wiki/Dermatofibrosarcoma_protuberans> ;
  onco:tag "subtype-page" ;
  onco:related <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/cancers/kaposi-sarcoma/> ;
  onco:technologies <https://onco.cc/terms/mohs-surgery/>, <https://onco.cc/technologies/kinase-inhibitors/>, <https://onco.cc/technologies/imrt-igrt/> ;
  onco:targets <https://onco.cc/targets/pdgfrb/>, <https://onco.cc/targets/pdgfra/> ;
  onco:drugs <https://onco.cc/drugs/imatinib/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/drugs/pazopanib/> ;
  onco:terms <https://onco.cc/terms/wide-local-excision/>, <https://onco.cc/terms/rare-cancers/> ;
  onco:pipeline <https://onco.cc/drugs/imatinib/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/drugs/pazopanib/> ;
  onco:standardOfCare <https://onco.cc/terms/mohs-surgery/>, <https://onco.cc/terms/wide-local-excision/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/drugs/imatinib/>, <https://onco.cc/targets/pdgfrb/>, <https://onco.cc/drugs/imatinib/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/doxorubicin/> .