# OnCo record desmoplastic-small-round-cell-tumour (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/desmoplastic-small-round-cell-tumour/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "desmoplastic-small-round-cell-tumour" ;
  schema:name "Desmoplastic small round cell tumour"@en ;
  schema:alternateName "DSRCT"@en, "Desmoplastic small round cell tumor"@en, "Intra-abdominal desmoplastic small round cell tumour"@en, "EWSR1-WT1 sarcoma"@en ;
  schema:description "Desmoplastic small round cell tumour is a very rare, aggressive sarcoma of adolescents and young men that grows across the lining of the abdomen as many nodules, driven by a fusion of the EWSR1 and WT1 genes. It is treated with intensive chemotherapy, surgery to remove every nodule, sometimes heated chemotherapy into the abdomen, and radiotherapy, yet most patients relapse within three years."@en ;
  schema:url <https://onco.cc/cancers/desmoplastic-small-round-cell-tumour/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Desmoplastic_small-round-cell_tumor> ;
  schema:citation <https://www.cancer.gov/types/soft-tissue-sarcoma/patient/child-soft-tissue-treatment-pdq>, <https://doi.org/10.1155/2014/680126>, <https://doi.org/10.3390/cancers13030498> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/cancers/ewing-sarcoma/>, <https://onco.cc/cancers/rhabdomyosarcoma/>, <https://onco.cc/cancers/peritoneal-mesothelioma/>, <https://onco.cc/cancers/childhood-cancers/>, <https://onco.cc/cancers/adamantinoma/> ;
  onco:technologies <https://onco.cc/technologies/hipec/> ;
  onco:targets <https://onco.cc/targets/wt1/>, <https://onco.cc/targets/pdgfra/> ;
  onco:drugs <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/ifosfamide/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/sunitinib/> ;
  onco:standardOfCare <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/ifosfamide/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/technologies/hipec/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/sunitinib/> .