# OnCo record epithelioid-haemangioendothelioma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/epithelioid-haemangioendothelioma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "epithelioid-haemangioendothelioma" ;
  schema:name "Epithelioid haemangioendothelioma"@en ;
  schema:alternateName "EHE"@en, "WWTR1-CAMTA1 sarcoma"@en, "YAP1-TFE3 haemangioendothelioma"@en ;
  schema:description "Epithelioid haemangioendothelioma is a rare vascular cancer driven by a fusion gene, usually WWTR1-CAMTA1, that behaves unpredictably: some tumours sit unchanged for years while others spread quickly. Stable disease is watched, localised tumours are removed, liver-only disease can be transplanted, and mTOR blockers such as sirolimus are the most used drugs when treatment is needed."@en ;
  schema:url <https://onco.cc/cancers/epithelioid-haemangioendothelioma/> ;
  schema:dateModified "2026-09-17"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Epithelioid_hemangioendothelioma> ;
  schema:citation <https://en.wikipedia.org/wiki/Epithelioid_hemangioendothelioma> ;
  onco:tag "subtype-page" ;
  onco:related <https://onco.cc/cancers/vascular-tumours/>, <https://onco.cc/cancers/angiosarcoma/> ;
  onco:pipeline <https://onco.cc/targets/mtor/>, <https://onco.cc/drugs/pazopanib/> ;
  onco:standardOfCare <https://onco.cc/technologies/active-surveillance/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/limb-salvage-surgery/>, <https://onco.cc/technologies/liver-transplant-oncology/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/targets/mtor/>, <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sirolimus-albumin-bound/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/paclitaxel/> .