# OnCo record esthesioneuroblastoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/esthesioneuroblastoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "esthesioneuroblastoma" ;
  schema:name "Esthesioneuroblastoma (olfactory neuroblastoma)"@en ;
  schema:alternateName "Olfactory neuroblastoma"@en, "ONB"@en, "Esthesioneuroepithelioma"@en, "Neuroblastoma of the olfactory epithelium"@en ;
  schema:description "Esthesioneuroblastoma is a rare cancer of the nasal cavity and sinuses that arises from the smell-sensing olfactory nerve lining at the roof of the nose, next to the brain. It is treated with surgery through the nose or skull base followed by radiotherapy, with chemotherapy added for high-grade or widespread tumours, and because it can return a decade or more later patients are followed for life."@en ;
  schema:url <https://onco.cc/cancers/esthesioneuroblastoma/> ;
  schema:dateModified "2026-09-18"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Esthesioneuroblastoma> ;
  schema:citation <https://www.nccn.org/guidelines/guidelines-detail?category=1&id=1437>, <https://en.wikipedia.org/wiki/Esthesioneuroblastoma> ;
  onco:tag "subtype-page", "head-and-neck" ;
  onco:related <https://onco.cc/cancers/sinonasal-undifferentiated-carcinoma/>, <https://onco.cc/cancers/sinonasal/>, <https://onco.cc/cancers/neuroblastoma/>, <https://onco.cc/cancers/nut-carcinoma/> ;
  onco:technologies <https://onco.cc/technologies/robotic-surgery/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/technologies/proton-therapy/>, <https://onco.cc/technologies/sstr-pet/>, <https://onco.cc/technologies/prrt/>, <https://onco.cc/technologies/radioligand-therapy/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/histopathology-ihc/> ;
  onco:targets <https://onco.cc/targets/sstr2/> ;
  onco:drugs <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/platinum-etoposide/>, <https://onco.cc/drugs/temozolomide/>, <https://onco.cc/drugs/lutathera/> ;
  onco:terms <https://onco.cc/terms/head-neck-subsites/>, <https://onco.cc/terms/rare-cancers/>, <https://onco.cc/terms/re-irradiation/>, <https://onco.cc/terms/staging-systems/>, <https://onco.cc/terms/chemoradiation/> ;
  onco:keyPapers <https://onco.cc/key-papers/paper-dulguerov-esthesioneuroblastoma-meta-analysis-lancet-oncol-2001/>, <https://onco.cc/key-papers/paper-kadish-olfactory-neuroblastoma-staging-cancer-1976/> ;
  onco:pipeline <https://onco.cc/technologies/proton-therapy/>, <https://onco.cc/drugs/lutathera/>, <https://onco.cc/technologies/prrt/> ;
  onco:standardOfCare <https://onco.cc/technologies/histopathology-ihc/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/sstr-pet/>, <https://onco.cc/technologies/pet-ct/>, <https://onco.cc/technologies/robotic-surgery/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/technologies/proton-therapy/>, <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/platinum-etoposide/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/terms/chemoradiation/>, <https://onco.cc/terms/re-irradiation/>, <https://onco.cc/drugs/lutathera/>, <https://onco.cc/technologies/prrt/>, <https://onco.cc/drugs/platinum-etoposide/>, <https://onco.cc/drugs/temozolomide/>, <https://onco.cc/technologies/mri/> .
