# OnCo record glucagonoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/glucagonoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "glucagonoma" ;
  schema:name "Glucagonoma"@en ;
  schema:alternateName "Glucagon-secreting pancreatic neuroendocrine tumour"@en, "Glucagonoma syndrome"@en, "Alpha-cell tumour of the pancreas"@en ;
  schema:description "Glucagonoma is a very rare pancreatic neuroendocrine tumour that pours out the hormone glucagon, causing weight loss, diabetes and a distinctive migrating red rash. Because the rash is so characteristic, spotting it early can lead to diagnosis before the tumour has spread to the liver; surgery is the definitive treatment and somatostatin analogues control the symptoms."@en ;
  schema:url <https://onco.cc/cancers/glucagonoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Glucagonoma> ;
  schema:citation <https://www.cancer.gov/types/pancreatic/neuroendocrine-tumors/treatment>, <https://doi.org/10.1111/j.1365-2265.2011.03967.x>, <https://doi.org/10.1111/jdv.13752> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/cancers/vipoma/>, <https://onco.cc/cancers/somatostatinoma/>, <https://onco.cc/cancers/men1-syndrome/>, <https://onco.cc/cancers/neuroendocrine/> ;
  onco:technologies <https://onco.cc/technologies/prrt/> ;
  onco:drugs <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/> ;
  onco:standardOfCare <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/technologies/prrt/> .
