# OnCo record intravascular-large-b-cell-lymphoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/intravascular-large-b-cell-lymphoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "intravascular-large-b-cell-lymphoma" ;
  schema:name "Intravascular large B-cell lymphoma"@en ;
  schema:alternateName "IVLBCL"@en, "Intravascular lymphoma"@en, "Angiotropic large cell lymphoma"@en, "Malignant angioendotheliomatosis"@en ;
  schema:description "Intravascular large B-cell lymphoma is a rare form of large B-cell lymphoma in which the cancer cells grow inside small blood vessels rather than forming lumps, so it causes fevers, confusion, skin patches or breathlessness and is often found late or only after death. Rituximab-based chemotherapy with drugs that reach the brain has turned a nearly always fatal disease into one often controlled."@en ;
  schema:url <https://onco.cc/cancers/intravascular-large-b-cell-lymphoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Intravascular_lymphomas> ;
  schema:citation <https://www.cancer.gov/types/lymphoma/patient/adult-nhl-treatment-pdq>, <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1016/s1470-2045(20)30059-0>, <https://doi.org/10.2147/cmar.s267825> ;
  onco:tag "subtype-page", "wave4", "haematologic", "rare" ;
  onco:related <https://onco.cc/cancers/dlbcl/>, <https://onco.cc/cancers/primary-cns-lymphoma/>, <https://onco.cc/cancers/lymphomatoid-granulomatosis/>, <https://onco.cc/cancers/hiv-associated-lymphoma/> ;
  onco:drugs <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/methotrexate/> ;
  onco:terms <https://onco.cc/terms/r-chop/>, <https://onco.cc/terms/myd88-l265p/> ;
  onco:standardOfCare <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/methotrexate/>, <https://onco.cc/terms/r-chop/>, <https://onco.cc/cancers/primary-cns-lymphoma/> .
