# OnCo record low-grade-appendiceal-mucinous-neoplasm (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/low-grade-appendiceal-mucinous-neoplasm/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "low-grade-appendiceal-mucinous-neoplasm" ;
  schema:name "Low-grade appendiceal mucinous neoplasm and pseudomyxoma peritonei"@en ;
  schema:alternateName "LAMN"@en, "Pseudomyxoma peritonei"@en, "PMP"@en, "Low-grade mucinous carcinoma peritonei"@en, "Disseminated peritoneal adenomucinosis"@en, "Jelly belly"@en ;
  schema:description "Low-grade appendiceal mucinous neoplasm is a slow-growing appendiceal cancer that makes mucus, and when it bursts it spreads jelly through the abdomen as pseudomyxoma peritonei. It rarely spreads through blood or lymph, so it is treated by stripping all visible disease from the abdomen and washing the cavity with heated chemotherapy, an operation that gives most patients many years of life."@en ;
  schema:url <https://onco.cc/cancers/low-grade-appendiceal-mucinous-neoplasm/> ;
  schema:dateModified "2026-09-18"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Pseudomyxoma_peritonei> ;
  schema:citation <https://doi.org/10.1200/JCO.2011.39.7166>, <https://doi.org/10.1097/PAS.0000000000000535>, <https://en.wikipedia.org/wiki/Pseudomyxoma_peritonei> ;
  onco:tag "subtype-page", "gastrointestinal" ;
  onco:related <https://onco.cc/cancers/appendiceal-adenocarcinoma/>, <https://onco.cc/cancers/goblet-cell-adenocarcinoma/>, <https://onco.cc/cancers/appendiceal/>, <https://onco.cc/cancers/peritoneal-mesothelioma/> ;
  onco:technologies <https://onco.cc/technologies/hipec/>, <https://onco.cc/technologies/hipec-pipac-devices/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/mri/> ;
  onco:targets <https://onco.cc/targets/kras/> ;
  onco:drugs <https://onco.cc/drugs/mitomycin/>, <https://onco.cc/drugs/folfox/>, <https://onco.cc/drugs/capox/> ;
  onco:terms <https://onco.cc/terms/hipec-procedure/>, <https://onco.cc/terms/peritoneal-metastasis/>, <https://onco.cc/terms/debulking/>, <https://onco.cc/terms/colectomy/>, <https://onco.cc/terms/peritoneum/> ;
  onco:keyPapers <https://onco.cc/key-papers/paper-psogi-pseudomyxoma-appendiceal-classification-am-j-surg-pathol-2016/>, <https://onco.cc/key-papers/paper-who-2019-digestive-system-tumours-nagtegaal-histopathology-2020/> ;
  onco:pipeline <https://onco.cc/technologies/hipec/>, <https://onco.cc/technologies/hipec-pipac-devices/> ;
  onco:standardOfCare <https://onco.cc/terms/colectomy/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/hipec/>, <https://onco.cc/terms/hipec-procedure/>, <https://onco.cc/drugs/mitomycin/>, <https://onco.cc/terms/peritoneal-metastasis/>, <https://onco.cc/terms/debulking/>, <https://onco.cc/technologies/hipec/>, <https://onco.cc/drugs/folfox/>, <https://onco.cc/drugs/capox/>, <https://onco.cc/terms/debulking/>, <https://onco.cc/technologies/hipec-pipac-devices/>, <https://onco.cc/drugs/folfox/> .