# OnCo record lymphomatoid-granulomatosis (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/lymphomatoid-granulomatosis/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "lymphomatoid-granulomatosis" ;
  schema:name "Lymphomatoid granulomatosis"@en ;
  schema:alternateName "LYG"@en, "EBV-positive B-cell lymphoproliferative disorder of the lung"@en, "Angiocentric immunoproliferative lesion"@en ;
  schema:description "Lymphomatoid granulomatosis is a rare Epstein-Barr virus-driven disease of B cells that invades and destroys blood vessels, almost always in the lungs and often the brain and skin, in people whose immune control of the virus is weak. Low-grade disease can be treated with interferon and high-grade disease as a large B-cell lymphoma with rituximab-based chemotherapy."@en ;
  schema:url <https://onco.cc/cancers/lymphomatoid-granulomatosis/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Lymphomatoid_granulomatosis> ;
  schema:citation <https://www.cancer.gov/types/lymphoma/patient/adult-nhl-treatment-pdq>, <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1097/pas.0b013e3181fd8781>, <https://doi.org/10.1097/pas.0000000000000328> ;
  onco:tag "subtype-page", "wave4", "haematologic", "rare" ;
  onco:related <https://onco.cc/cancers/non-hodgkin-lymphoma/>, <https://onco.cc/cancers/dlbcl/>, <https://onco.cc/cancers/intravascular-large-b-cell-lymphoma/>, <https://onco.cc/cancers/post-transplant-lymphoproliferative-disorder/>, <https://onco.cc/cancers/hiv-associated-lymphoma/> ;
  onco:drugs <https://onco.cc/drugs/interferon-alfa/>, <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/cyclophosphamide/> ;
  onco:standardOfCare <https://onco.cc/drugs/interferon-alfa/>, <https://onco.cc/cancers/non-hodgkin-lymphoma/>, <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/cancers/dlbcl/> .
