# OnCo record pancreatoblastoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/pancreatoblastoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "pancreatoblastoma" ;
  schema:name "Pancreatoblastoma"@en ;
  schema:alternateName "Infantile pancreatic carcinoma"@en, "Childhood pancreatic cancer"@en, "Paediatric pancreatoblastoma"@en ;
  schema:description "Pancreatoblastoma is the pancreatic cancer of young children, a tumour of immature pancreatic cells that behaves quite unlike adult pancreatic cancer. It grows as a large abdominal mass, often raises the blood marker alpha-fetoprotein, and is treated like the childhood liver cancer hepatoblastoma: chemotherapy to shrink it, then surgery, which cures most children whose tumour has not spread."@en ;
  schema:url <https://onco.cc/cancers/pancreatoblastoma/> ;
  schema:dateModified "2026-09-18"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Pancreatoblastoma> ;
  schema:citation <https://en.wikipedia.org/wiki/Pancreatoblastoma>, <https://doi.org/10.1002/pbc.29112> ;
  onco:tag "subtype-page", "gastrointestinal" ;
  onco:related <https://onco.cc/cancers/pancreatic-acinar-cell-carcinoma/>, <https://onco.cc/cancers/resectable-pdac/>, <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/cancers/hepatoblastoma/>, <https://onco.cc/cancers/rare-childhood-cancers/>, <https://onco.cc/cancers/childhood-cancers/> ;
  onco:technologies <https://onco.cc/technologies/cytotoxic-chemotherapy/>, <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/germline-testing/>, <https://onco.cc/technologies/fertility-preservation/> ;
  onco:targets <https://onco.cc/targets/kras/> ;
  onco:drugs <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/vincristine/> ;
  onco:pathways <https://onco.cc/pathways/wnt/>, <https://onco.cc/pathways/pancreatic-cancer-signalling/> ;
  onco:terms <https://onco.cc/terms/whipple/>, <https://onco.cc/terms/resection-margins/>, <https://onco.cc/terms/neoadjuvant-adjuvant/>, <https://onco.cc/terms/metastasis/>, <https://onco.cc/terms/tumour-grade/> ;
  onco:standardOfCare <https://onco.cc/technologies/ct/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/germline-testing/>, <https://onco.cc/terms/whipple/>, <https://onco.cc/terms/resection-margins/>, <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/terms/neoadjuvant-adjuvant/>, <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/terms/metastasis/>, <https://onco.cc/technologies/fertility-preservation/>, <https://onco.cc/terms/cachexia/> .
