# OnCo record pineoblastoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/pineoblastoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "pineoblastoma" ;
  schema:name "Pineoblastoma"@en ;
  schema:alternateName "Pineal embryonal tumour"@en, "Pineoblastoma (WHO grade 4)"@en, "Trilateral retinoblastoma (pineoblastoma with bilateral retinoblastoma)"@en ;
  schema:description "Pineoblastoma is a rare, aggressive brain tumour of the pineal gland, mostly in children, made of primitive cells like those of medulloblastoma. It is treated with surgery, radiotherapy to the whole brain and spine in children old enough, and chemotherapy; infants do worst, and molecular subgroups discovered in 2020, including ones linked to the DICER1 gene, are starting to guide treatment."@en ;
  schema:url <https://onco.cc/cancers/pineoblastoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Pineoblastoma> ;
  schema:citation <https://www.cancer.gov/types/brain/patient/child-cns-embryonal-treatment-pdq>, <https://doi.org/10.1007/s00401-019-02111-y>, <https://doi.org/10.1093/noajnl/vdac056> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/brain-tumours/>, <https://onco.cc/cancers/medulloblastoma/>, <https://onco.cc/cancers/pineal-parenchymal-tumours/>, <https://onco.cc/cancers/papillary-tumour-pineal-region/>, <https://onco.cc/cancers/retinoblastoma/>, <https://onco.cc/cancers/pleuropulmonary-blastoma-dicer1/> ;
  onco:targets <https://onco.cc/targets/dicer1/> ;
  onco:drugs <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/carboplatin/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/cyclophosphamide/> ;
  onco:standardOfCare <https://onco.cc/cancers/brain-tumours/>, <https://onco.cc/cancers/medulloblastoma/>, <https://onco.cc/drugs/cisplatin/>, <https://onco.cc/drugs/carboplatin/>, <https://onco.cc/drugs/vincristine/> .
