# OnCo record primary-cutaneous-marginal-zone-lymphoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/primary-cutaneous-marginal-zone-lymphoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "primary-cutaneous-marginal-zone-lymphoma" ;
  schema:name "Primary cutaneous marginal zone lymphoma"@en ;
  schema:alternateName "Primary cutaneous marginal zone B-cell lymphoma"@en, "Primary cutaneous marginal zone lymphoproliferative disorder"@en, "Primary cutaneous immunocytoma"@en, "Cutaneous immunocytoma"@en, "PCMZL"@en ;
  schema:description "Primary cutaneous marginal zone lymphoma is a very slow-growing lymphoma that appears as pink or purple lumps in the skin, usually on the arms or trunk, and almost never spreads inside the body. WHO-HAEM5 now calls it a lymphoproliferative disorder because it behaves so well; surgery or radiotherapy clears most lesions, and relapses in the skin are common but harmless."@en ;
  schema:url <https://onco.cc/cancers/primary-cutaneous-marginal-zone-lymphoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Primary_cutaneous_marginal_zone_lymphoma> ;
  schema:citation <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1016/j.jaad.2013.04.047>, <https://doi.org/10.1038/modpathol.2013.106>, <https://doi.org/10.1016/j.annonc.2019.10.010> ;
  onco:tag "subtype-page", "wave4", "haematologic", "rare" ;
  onco:related <https://onco.cc/cancers/marginal-zone-lymphoma/>, <https://onco.cc/cancers/malt-lymphoma/>, <https://onco.cc/cancers/primary-cutaneous-follicle-centre-lymphoma/>, <https://onco.cc/cancers/cutaneous-t-cell-lymphoma/> ;
  onco:drugs <https://onco.cc/drugs/rituximab/> ;
  onco:standardOfCare <https://onco.cc/cancers/marginal-zone-lymphoma/>, <https://onco.cc/drugs/rituximab/>, <https://onco.cc/cancers/marginal-zone-lymphoma/> .
