# OnCo record primary-effusion-lymphoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/primary-effusion-lymphoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "primary-effusion-lymphoma" ;
  schema:name "Primary effusion lymphoma"@en ;
  schema:alternateName "PEL"@en, "Body cavity-based lymphoma"@en, "Extracavitary primary effusion lymphoma"@en, "KSHV/HHV8-associated lymphoma"@en, "HHV8-positive primary effusion lymphoma"@en ;
  schema:description "A rare lymphoma that grows as fluid rather than as a lump: it fills the space around the lungs, the heart or the bowel without forming a mass. It is caused by Kaposi sarcoma herpesvirus and arises mostly in people with advanced HIV infection, and it is diagnosed by sending the fluid itself for testing."@en ;
  schema:url <https://onco.cc/cancers/primary-effusion-lymphoma/> ;
  schema:dateModified "2026-09-29"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Primary_effusion_lymphoma> ;
  schema:citation <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1182/blood.2022015851>, <https://doi.org/10.1002/hon.70168>, <https://www.cancer.gov/types/lymphoma/hp/adult-nhl-treatment-pdq> ;
  onco:tag "heme", "lymphoma", "subtype-page" ;
  onco:related <https://onco.cc/cancers/hiv-associated-lymphoma/>, <https://onco.cc/cancers/dlbcl/>, <https://onco.cc/cancers/plasmablastic-lymphoma/>, <https://onco.cc/cancers/non-hodgkin-lymphoma/>, <https://onco.cc/cancers/kaposi-sarcoma/> ;
  onco:technologies <https://onco.cc/technologies/histopathology-ihc/> ;
  onco:terms <https://onco.cc/terms/hhv8-kshv/>, <https://onco.cc/terms/ebv-term/>, <https://onco.cc/terms/lymphoma-classification-2022/>, <https://onco.cc/terms/lymphoma-nodal-versus-extranodal/>, <https://onco.cc/pathways/oncogenic-viruses/> ;
  onco:standardOfCare <https://onco.cc/terms/hhv8-kshv/>, <https://onco.cc/terms/ebv-term/>, <https://onco.cc/technologies/histopathology-ihc/>, <https://onco.cc/terms/lymphoma-classification-2022/>, <https://onco.cc/cancers/hiv-associated-lymphoma/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/terms/lymphoma-tx-regimen-alphabet/> .
