# OnCo record sdh-deficient-renal-cell-carcinoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/sdh-deficient-renal-cell-carcinoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "sdh-deficient-renal-cell-carcinoma" ;
  schema:name "Succinate dehydrogenase-deficient renal cell carcinoma"@en ;
  schema:alternateName "SDH-deficient renal cell carcinoma"@en, "SDHB-deficient renal cell carcinoma"@en, "Succinate dehydrogenase-deficient RCC"@en ;
  schema:description "Succinate dehydrogenase-deficient renal cell carcinoma is a very rare kidney cancer of younger adults who carry a faulty SDH gene, the same fault that causes hereditary paraganglioma and some stomach stromal tumours. Most are low grade and cured by surgery, but a minority spread years later, so patients and relatives need gene testing and follow-up."@en ;
  schema:url <https://onco.cc/cancers/sdh-deficient-renal-cell-carcinoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Renal_cell_carcinoma> ;
  schema:citation <https://doi.org/10.1016/j.eururo.2016.02.029>, <https://doi.org/10.1016/j.eururo.2022.06.016>, <https://doi.org/10.1038/modpathol.2014.86>, <https://doi.org/10.1111/his.13183> ;
  onco:tag "subtype-page", "wave4", "kidney", "rare" ;
  onco:related <https://onco.cc/cancers/rcc/>, <https://onco.cc/cancers/fh-deficient-renal-cell-carcinoma/>, <https://onco.cc/cancers/hereditary-ppgl/>, <https://onco.cc/cancers/chromophobe-rcc/>, <https://onco.cc/cancers/gist/> ;
  onco:technologies <https://onco.cc/technologies/germline-testing/> ;
  onco:targets <https://onco.cc/targets/sdhb/> ;
  onco:terms <https://onco.cc/terms/nephrectomy/>, <https://onco.cc/terms/hereditary-cancer-syndromes/> ;
  onco:standardOfCare <https://onco.cc/cancers/rcc/>, <https://onco.cc/technologies/germline-testing/>, <https://onco.cc/terms/nephrectomy/>, <https://onco.cc/cancers/hereditary-ppgl/> .
