# OnCo record solid-pseudopapillary-neoplasm (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/solid-pseudopapillary-neoplasm/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "solid-pseudopapillary-neoplasm" ;
  schema:name "Solid pseudopapillary neoplasm of the pancreas"@en ;
  schema:alternateName "Solid pseudopapillary neoplasm (young women; CTNNB1; low-grade malignant; cured by resection in about 95 percent)"@en, "Solid pseudopapillary tumour"@en, "SPN"@en, "SPT"@en, "Frantz tumour"@en, "Hamoudi tumour"@en, "Papillary cystic neoplasm of the pancreas"@en, "Solid and papillary epithelial neoplasm"@en ;
  schema:description "Solid pseudopapillary neoplasm is a rare, slow-growing pancreatic tumour of young women that is classed as a low-grade cancer. It is driven by a fault in the beta-catenin gene rather than the KRAS mutation of ordinary pancreatic cancer, is often found by chance as a large mass, and surgery cures more than nineteen in twenty patients, although it can recur years later."@en ;
  schema:url <https://onco.cc/cancers/solid-pseudopapillary-neoplasm/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Solid_pseudopapillary_tumour> ;
  schema:citation <https://doi.org/10.1097/mpa.0000000000000061>, <https://doi.org/10.1016/s0002-9440(10)62563-1>, <https://doi.org/10.1111/his.13975>, <https://www.cancerresearchuk.org/about-cancer/pancreatic-cancer/stages-types-grades/types> ;
  onco:tag "gi", "pancreatic", "subtype-page" ;
  onco:related <https://onco.cc/cancers/pancreatic/>, <https://onco.cc/cancers/pancreatoblastoma/>, <https://onco.cc/cancers/pancreatic-acinar-cell-carcinoma/>, <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/cancers/ipmn-cystic-precursors/>, <https://onco.cc/cancers/mcn-associated-carcinoma/> ;
  onco:technologies <https://onco.cc/technologies/robotic-surgery/>, <https://onco.cc/technologies/histopathology-ihc/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/technologies/ct/> ;
  onco:targets <https://onco.cc/targets/kras/> ;
  onco:pathways <https://onco.cc/pathways/wnt/>, <https://onco.cc/pathways/pancreatic-cancer-signalling/> ;
  onco:terms <https://onco.cc/terms/distal-pancreatectomy/>, <https://onco.cc/terms/whipple/>, <https://onco.cc/terms/tumour-grade/>, <https://onco.cc/terms/oligometastatic/> ;
  onco:standardOfCare <https://onco.cc/terms/distal-pancreatectomy/>, <https://onco.cc/terms/whipple/>, <https://onco.cc/technologies/robotic-surgery/>, <https://onco.cc/technologies/mri/>, <https://onco.cc/terms/oligometastatic/>, <https://onco.cc/terms/distal-pancreatectomy/> .
