# OnCo record somatostatinoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/somatostatinoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "somatostatinoma" ;
  schema:name "Somatostatinoma"@en ;
  schema:alternateName "Somatostatin-secreting neuroendocrine tumour"@en, "Duodenal somatostatinoma"@en, "Delta-cell tumour"@en, "Inhibitory syndrome tumour"@en ;
  schema:description "Somatostatinoma is one of the rarest neuroendocrine tumours, arising in the pancreas or the duodenum and secreting somatostatin, a hormone that switches off digestion, which can cause mild diabetes, gallstones and fatty diarrhoea. Duodenal cases are often linked to neurofibromatosis type 1 and rarely cause symptoms. Surgery is the main treatment and the outlook depends on site and grade."@en ;
  schema:url <https://onco.cc/cancers/somatostatinoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Somatostatinoma> ;
  schema:citation <https://www.cancer.gov/types/pancreatic/neuroendocrine-tumors/treatment>, <https://doi.org/10.1111/j.1440-1746.2007.05053.x>, <https://doi.org/10.3892/etm.2020.8965> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/cancers/glucagonoma/>, <https://onco.cc/cancers/vipoma/>, <https://onco.cc/cancers/small-intestinal-net/>, <https://onco.cc/cancers/men1-syndrome/> ;
  onco:technologies <https://onco.cc/technologies/prrt/> ;
  onco:targets <https://onco.cc/targets/nf1/> ;
  onco:drugs <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/> ;
  onco:standardOfCare <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/technologies/prrt/> .
