# OnCo record splenic-marginal-zone-lymphoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/splenic-marginal-zone-lymphoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "splenic-marginal-zone-lymphoma" ;
  schema:name "Splenic marginal zone lymphoma"@en ;
  schema:alternateName "SMZL"@en, "Splenic lymphoma with villous lymphocytes"@en, "Splenic marginal zone B-cell lymphoma"@en ;
  schema:description "Splenic marginal zone lymphoma is a slow-growing lymphoma that grows in the spleen and bone marrow, causing a very large spleen and a raised lymphocyte count but rarely swollen lymph nodes. Many people need no treatment for years; when they do, rituximab has largely replaced removal of the spleen, and hepatitis C should be treated first where it is present."@en ;
  schema:url <https://onco.cc/cancers/splenic-marginal-zone-lymphoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Splenic_marginal_zone_lymphoma> ;
  schema:citation <https://www.cancer.gov/types/lymphoma/patient/adult-nhl-treatment-pdq>, <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1016/j.annonc.2019.10.010>, <https://doi.org/10.1016/j.bjhh.2016.09.014>, <https://doi.org/10.1038/s41598-019-46906-1> ;
  onco:tag "subtype-page", "wave4", "haematologic", "rare" ;
  onco:related <https://onco.cc/cancers/marginal-zone-lymphoma/>, <https://onco.cc/cancers/malt-lymphoma/>, <https://onco.cc/cancers/nodal-marginal-zone-lymphoma/>, <https://onco.cc/cancers/hairy-cell-leukemia/>, <https://onco.cc/cancers/splenic-b-cell-lymphoma-leukaemia-prominent-nucleoli/> ;
  onco:drugs <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/bendamustine/>, <https://onco.cc/drugs/zanubrutinib/>, <https://onco.cc/drugs/lenalidomide/> ;
  onco:trials <https://onco.cc/trials/augment/> ;
  onco:standardOfCare <https://onco.cc/cancers/marginal-zone-lymphoma/>, <https://onco.cc/drugs/rituximab/>, <https://onco.cc/drugs/bendamustine/>, <https://onco.cc/drugs/zanubrutinib/>, <https://onco.cc/drugs/lenalidomide/>, <https://onco.cc/trials/augment/> .
