# OnCo record vipoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/vipoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "vipoma" ;
  schema:name "VIPoma"@en ;
  schema:alternateName "Vasoactive intestinal peptide-secreting tumour"@en, "Verner-Morrison syndrome"@en, "Pancreatic cholera"@en, "WDHA syndrome (watery diarrhoea, hypokalaemia, achlorhydria)"@en ;
  schema:description "VIPoma is a very rare pancreatic neuroendocrine tumour that secretes vasoactive intestinal peptide, causing litres of watery diarrhoea a day with dangerous loss of potassium. Most have spread to the liver by diagnosis. Fluid replacement and somatostatin analogues control the diarrhoea, surgery cures the few caught early, and the usual neuroendocrine tumour treatments are used for spread."@en ;
  schema:url <https://onco.cc/cancers/vipoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/VIPoma> ;
  schema:citation <https://www.cancer.gov/types/pancreatic/neuroendocrine-tumors/treatment>, <https://doi.org/10.1016/j.pan.2021.08.001> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/cancers/glucagonoma/>, <https://onco.cc/cancers/somatostatinoma/>, <https://onco.cc/cancers/men1-syndrome/>, <https://onco.cc/cancers/neuroendocrine/> ;
  onco:technologies <https://onco.cc/technologies/prrt/> ;
  onco:drugs <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/> ;
  onco:standardOfCare <https://onco.cc/cancers/pancreatic-net/>, <https://onco.cc/drugs/everolimus/>, <https://onco.cc/drugs/sunitinib/>, <https://onco.cc/technologies/prrt/> .
