# OnCo record wilms-tumor (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix owl: <http://www.w3.org/2002/07/owl#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/wilms-tumor/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "wilms-tumor" ;
  schema:name "Wilms tumour (nephroblastoma)"@en ;
  schema:description "Wilms tumour is a kidney cancer of young children and one of paediatric oncology's success stories: surgery plus a few months of chemotherapy cures about nine in ten. Today's trials aim to give the lowest-risk children almost no chemotherapy while finding the few with aggressive biology."@en ;
  schema:url <https://onco.cc/cancers/wilms-tumor/> ;
  schema:dateModified "2026-09-08"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Wilms%27_tumor> ;
  owl:sameAs <http://www.wikidata.org/entity/Q756289> ;
  schema:citation <https://www.cancer.gov/types/kidney/patient/wilms-treatment-pdq>, <https://doi.org/10.1038/nrurol.2017.163>, <https://childrensoncologygroup.org/> ;
  onco:tag "gap-fill", "paediatric" ;
  onco:related <https://onco.cc/roadmaps/paediatric-oncology-roadmap/>, <https://onco.cc/cancers/neuroblastoma/>, <https://onco.cc/cancers/hepatoblastoma/>, <https://onco.cc/cancers/retinoblastoma/>, <https://onco.cc/cancers/pleuropulmonary-blastoma/> ;
  onco:technologies <https://onco.cc/technologies/cytotoxic-chemotherapy/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/technologies/robotic-surgery/>, <https://onco.cc/technologies/germline-testing/>, <https://onco.cc/technologies/survivorship-care-plan/>, <https://onco.cc/technologies/ultrasound/> ;
  onco:targets <https://onco.cc/targets/tp53/> ;
  onco:drugs <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/dactinomycin/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/carboplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/ifosfamide/> ;
  onco:companies <https://onco.cc/companies/childrens-oncology-group/> ;
  onco:pathways <https://onco.cc/pathways/wnt/>, <https://onco.cc/pathways/p53-cell-cycle/> ;
  onco:terms <https://onco.cc/terms/germline-vs-somatic/>, <https://onco.cc/terms/nephrectomy/>, <https://onco.cc/terms/wilms-risk-markers/> ;
  onco:trials <https://onco.cc/trials/ccss/>, <https://onco.cc/trials/aren0532/> ;
  onco:people <https://onco.cc/people/jeffrey-dome/> ;
  onco:keyPapers <https://onco.cc/key-papers/paper-van-den-heuvel-eibrink-nat-rev-urol/> ;
  onco:journals <https://onco.cc/journals/journal-of-pediatric-hematology-oncology/>, <https://onco.cc/journals/pediatric-hematology-and-oncology/> ;
  onco:pipeline <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/dactinomycin/> ;
  onco:standardOfCare <https://onco.cc/technologies/active-surveillance/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/dactinomycin/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/dactinomycin/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/technologies/imrt-igrt/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/carboplatin/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/ifosfamide/> .
