OnCo

Chordoma: lines of therapy

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3 standard-of-care settings across 3 lines and 2 biomarker subgroups. Rows come from the cancer page's standard of care; the grid places each on its line and subgroup.

LineAll comersEGFR
Early / localised1·
Locally advanced1·
Advanced, first line·1

Early / localised

SubgroupSettingApproachProducts and trialsEvidence
All comersResectable, any siteEn bloc resection with negative margins by a spine or skull-base team, followed by high-dose proton or carbon-ion radiotherapy; intralesional surgery is associated with early recurrence.91

Locally advanced

SubgroupSettingApproachProducts and trialsEvidence
All comersUnresectable or medically inoperableDefinitive particle therapy (proton or carbon-ion) to 70 Gy-equivalent or higher; stereotactic photon radiosurgery where particles are unavailable.40

Advanced, first line

SubgroupSettingApproachProducts and trialsEvidence
EGFRAdvanced or metastaticClinical trial preferred. Imatinib (PDGFRB-positive), afatinib or other EGFR inhibitors, or sorafenib give mainly disease stabilisation; tazemetostat for INI1-negative poorly differentiated chordoma.97

Lines and subgroups are parsed from the setting text of each standard-of-care row and can misclassify an unusual phrasing; the row’s own setting is always shown. Guideline chips reflect the NCCN category and ESMO-MCBS grade recorded on the cancer page, checked on its stated date. Not medical advice.