OnCo

Rare cancers of childhood (NCI PDQ umbrella): lines of therapy

Cancer page →

3 standard-of-care settings across 2 lines and 1 biomarker subgroup. Rows come from the cancer page's standard of care; the grid places each on its line and subgroup.

LineAll comers
Second line1
Other settings2

Second line

SubgroupSettingApproachProducts and trialsEvidence
All comersRecurrent respiratory papillomatosisRepeated microdebrider or laser debulking to maintain the airway; systemic bevacizumab for severe refractory disease; HPV vaccination (prevention through maternal vaccination; adjuvant use under study).98

Other settings

SubgroupSettingApproachProducts and trialsEvidence
All comersCardiac rhabdomyoma with tuberous sclerosisObservation for spontaneous regression; mTOR inhibitor (everolimus or sirolimus) for haemodynamically significant tumours; surgery reserved for obstruction unresponsive to medical therapy.95
All comersAdult-type carcinoma in a childTreat per the adult site-specific standard with paediatric dose adjustment, enrol in the COG or EXPeRT rare tumour registry, and test for germline predisposition.94

Lines and subgroups are parsed from the setting text of each standard-of-care row and can misclassify an unusual phrasing; the row’s own setting is always shown. Guideline chips reflect the NCCN category and ESMO-MCBS grade recorded on the cancer page, checked on its stated date. Not medical advice.