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Cancers
Fumarate hydratase-deficient renal cell carcinoma (HLRCC-associated)
Data

Cancers·Fumarate hydratase-deficient renal cell carcinoma (HLRCC-associated)

DataFumarate hydratase-deficient renal cell carcinoma (HLRCC-associated)

Back to the Fumarate hydratase-deficient renal cell carcinoma hub →4 connected records

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Overview What it is Finding it Treating it Evidence The science Where you are Living with it What is coming Data

Data

Related pages

4

Direct links plus the targets, companies, and technologies of this cancer's products.

Similar pages

not linked directly; found by shared links

Cancer
Renal medullary carcinoma (SMARCB1-deficient)
Shares Collecting duct carcinoma of the kidney, Nephrectomy, Papillary renal cell carcinoma, Renal cell carcinoma and the tags subtype-page, wave4, kidney, rare.
Cancer
Eosinophilic solid and cystic renal cell carcinoma
Shares Succinate dehydrogenase-deficient renal cell carcinoma, Nephrectomy, Renal cell carcinoma and the tags subtype-page, wave4, kidney, rare.
Cancer
Clear cell papillary renal cell tumour
Shares Nephrectomy, Papillary renal cell carcinoma, Renal cell carcinoma and the tags subtype-page, wave4, kidney, rare.
Cancer
Mucinous tubular and spindle cell carcinoma of the kidney
Shares Nephrectomy, Papillary renal cell carcinoma, Renal cell carcinoma and the tags subtype-page, wave4, kidney, rare.
Cancer
TFE3-rearranged (translocation) renal cell carcinoma
Shares Collecting duct carcinoma of the kidney, Papillary renal cell carcinoma, Renal cell carcinoma and the tags subtype-page, wave4, kidney, rare.
Cancer
Multiple endocrine neoplasia type 2 (MEN2A and MEN2B)
Shares Hereditary pheochromocytoma and paraganglioma (SDHx, VHL, RET, NF1, MAX and TMEM127), Hereditary cancer syndromes, Germline (hereditary) testing and the tags subtype-page, wave4, rare.
Cancer
Hyperparathyroidism-jaw tumour syndrome (CDC73-related parathyroid carcinoma)
Shares Hereditary cancer syndromes, Germline (hereditary) testing and the tags subtype-page, wave4, rare.
Cancer
Multiple endocrine neoplasia type 1 (MEN1)
Shares Hereditary cancer syndromes, Germline (hereditary) testing and the tags subtype-page, wave4, rare.

technologies

1

Germline (hereditary) testing

targets

1

terms

2

Hereditary cancer syndromes Nephrectomy

Machine-readable versions

The same record for scripts and assistants; checked 2026-09-24. Data CC BY-NC 4.0, attribute “Data from OnCo (onco.cc)”.

JSON with neighbours Markdown context RDF Turtle Sections with routes and counts API root

Not yet reviewedNeeds expert (clinical) and patient advocate review. Review this page or see the review queue and roster.

Model panel commentary is coming to this page: machine commentary, not clinical review.

Wikipedia

Hereditary leiomyomatosis and renal cell cancer syndrome

Sources & links

NCI PDQ: renal cell cancer treatment
Moch 2016, European Urology: the 2016 WHO classification of urinary and male genital tumours, part A
Moch 2022, European Urology: the 2022 WHO classification of urinary and male genital tumours, part A (renal, penile, testicular)
Am J Surg Pathol 2016: fumarate hydratase-deficient RCC is strongly correlated with FH mutation and HLRCC
Am J Surg Pathol 2016: tubulocystic carcinoma with poorly differentiated foci, a pattern of FH-deficient RCC
Histopathology 2017: a low-grade oncocytic FH-deficient RCC resembling SDH-deficient RCC

subtype-page wave4 kidney rare

Data

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Machine-readable versions of Fumarate hydratase-deficient renal cell carcinoma (HLRCC-associated)

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MCP server: npx -y onco-mcp, tools search, get_entity, list_kind, ask, context, compare. This record is get_entity or context with id fh-deficient-renal-cell-carcinoma.

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