OnCo

Mismatch repair proteins (MLH1, MSH2, MSH6, PMS2)

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The four mismatch repair proteins proofread newly copied DNA; when a tumour loses one of them its DNA fills with small errors, and that state (dMMR or MSI-high) is what lets immunotherapy work across many cancers. This dossier gathers the 0 products (0 approved), 0 trials, 0 pathways and 0 resistance routes in the corpus that involve it, with external identifiers so it can be joined to UniProt, ChEMBL, Open Targets and the rest of biology.

Biology

Deficient repair raises the mutation rate a hundredfold and produces frameshift neoantigens in repeat-containing genes, which is the mechanistic basis for checkpoint inhibitor sensitivity.

Where it is found
  • Colorectal cancer (about 15 percent, most sporadic through MLH1 methylation)
  • Endometrial cancer (about 25 to 30 percent)
  • Gastric, small bowel, urothelial and other Lynch-spectrum tumours
Class: enzyme · Gene: MLH1, MSH2, MSH6, PMS2 · Facts checked 2026-09-23 · Target page

External identifiers

Built from HGNC, Ensembl, UniProt and ChEMBL ids

Products by modality and phase

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No trial in the corpus names this target or one of its products.

Resistance routes

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The resistance atlas has no route that names this target.

No pathway diagram carries this target as a node.

Companion diagnostics

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Preclinical models

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No model entry for this target yet; check the cancer entries on the models page.

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Literature

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Query for this target: (TITLE:"Mismatch repair proteins" OR ABSTRACT:"Mismatch repair proteins" OR TITLE:"MLH1, MSH2, MSH6, PMS2" OR ABSTRACT:"MLH1, MSH2, MSH6, PMS2" OR TITLE:"MLH1" OR ABSTRACT:"MLH1" OR TITLE:"MSH2" OR ABSTRACT:"MSH2" OR TITLE:"MSH6" OR ABSTRACT:"MSH6" OR TITLE:"PMS2" OR ABSTRACT:"PMS2") AND (cancer OR tumor OR tumour OR oncology OR carcinoma OR lymphoma OR leukemia OR leukaemia OR myeloma OR sarcoma OR melanoma OR glioma). Results are unfiltered search hits about Mismatch repair proteins (MLH1, MSH2, MSH6, PMS2), not a curated reading list.

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The dossier as machine-readable JSON: identifiers from HGNC, Ensembl, UniProt and ChEMBL, products with status, trials, pathways, hotspots, open questions and assays. The full entity record is in the open API at /api/v1/entities/mmr.json. Licence CC BY-NC 4.0.